Scleroderma

What’s Your Rare iQ?

One form of scleroderma is called CREST. What condition does the R in CREST represent?

Hemophagocytic lymphohistiocytosis (HLH)

Rare View

60% of tuberous sclerosis cases are diagnosed in the first year. Diagnosis slows down considerably after the first year.

Measured by: prevalence

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Disease	Estimated US Prevalence	Onset Image
Uveitis/a>	100,000-135,000
Sjogren's syndrome	140,000-374,000
Polymyositis	16,000-42,000
Systemic lupus erythematosus	161,000-322,000
Bullous pemphigoid	35,000-50,000
Lupus nephritis	66,500-124,000
Scleroderma	75,000-85,000
Behcet's disease	9,000-17,200