The Rare Disease Database

The most comprehensive source of rare disease information.

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Top 10 rare rheumatological diseases

Measured by: prevalence

Disease
Estimated US PrevalenceInheritanceAge of Onset
Systemic lupus erythematosus161,000-322,000
Sjogren's syndrome140,000-374,000
Uveitis100,000-135,000
Autoimmune hepatitis85,000-102,500
Scleroderma75,000-85,000
Lupus nephritis66,500-124,000
Bullous pemphigoid35,000-50,000
Polymyositis16,000-42,000
Behcet's disease9,000-17,200